Fibrous Dysplasia

FACTS

 

HPI

 

PHYSICAL EXAM


IMAGING

 

A/P
 
Figure 1: Growing Painless Vertex Fibrous Dysplasia in Healthy Adolescent with a right vertex fibrous dysplasia with minimal T1 hyperintensity (A) and diffuse hetergenous enhancement (B) with inner and outer table invasion and sagittal sinus abutment (C), underwent a bilateral parietal crani for gross total excision of lesion with 1cm margins circumferentially, and a titanium mesh cranioplasty (D). Final pathology demonstrated foci of bland-appearing fibroblasts admixed with irregular trabeculae of woven bone, areas of cystic change (pseudocyst appearance with no cyst lining), overall consistent with a diagnosis of FD. Intra-operatively, there was no soft tissue invasion.
Figure 1: Growing Painless Vertex Fibrous Dysplasia in Healthy Adolescent with a right vertex fibrous dysplasia with minimal T1 hyperintensity (A) and diffuse hetergenous enhancement (B) with inner and outer table invasion and sagittal sinus abutment (C), underwent a bilateral parietal crani for gross total excision of lesion with 1cm margins circumferentially, and a titanium mesh cranioplasty (D). Final pathology demonstrated foci of bland-appearing fibroblasts admixed with irregular trabeculae of woven bone, areas of cystic change (pseudocyst appearance with no cyst lining), overall consistent with a diagnosis of FD. Intra-operatively, there was no soft tissue invasion.